Behavioural Features of Italian Infants and Young Adults with Williams-Beuren Syndrome

Autor/inn/en	Gagliardi, C.; Martelli, S.; Tavano, A.; Borgatti, R.
Titel	Behavioural Features of Italian Infants and Young Adults with Williams-Beuren Syndrome
Quelle	In: Journal of Intellectual Disability Research, 55 (2011) 2, S.121-131 (11 Seiten)Infoseite zur Zeitschrift PDF als Volltext Verfügbarkeit
Sprache	englisch
Dokumenttyp	gedruckt; online; Zeitschriftenaufsatz
ISSN	0964-2633
DOI	10.1111/j.1365-2788.2010.01376.x
Schlagwörter	Emotional Problems; Mental Retardation; Young Adults; Interpersonal Relationship; Interaction; Empathy; Anxiety; Cognitive Ability; Infants; Genetic Disorders; Questionnaires; Gender Differences; Age Differences; Behavior Problems; Attention Span; Foreign Countries; Italy + Suchen Sie Ihr Suchwort? Geistige Behinderung; Young adult; Junger Erwachsener; Interpersonal relation; Interpersonal relations; Interpersonelle Beziehung; Zwischenmenschliche Beziehung; Interaktion; Empathie; Angst; Denkfähigkeit; Infant; Toddler; Toddlers; Kleinkind; Fragebogen; Geschlechterkonflikt; Age; Difference; Age difference; Altersunterschied; Ausland; Italien
Abstract	Background: The increased interest in social interaction in Williams-Beuren syndrome (WBS) is evident from infancy onwards, together not only with increased empathy, positive interpersonal bias, but also with social disinhibition. Previous studies have described behavioural and emotional problems as being widely represented in WBS. There is limited scope for comparisons between literature data because of the variety of instruments used to assess behaviour. Method: Forty-one children and young adults with WBS were enrolled and underwent general cognitive assessment. In order to compare our data with the literature, we used standardised questionnaires used in previous studies (Developmental Behaviour Checklist: DBC-P). General cognitive abilities, gender and age were included in the analysis. Results: Behavioural problems were more relevant than expected according to intellectual impairment. Some features were present at any age: inattention, anxiety, disruptive behaviours. Antisocial conduct was almost absent; perseverative conduct, a poor sense of danger and, more generally, self-absorbed behaviours tended to diminish along with age and to be linked to more pronounced cognitive impairment. Conclusion: As previously described for other countries, behaviour disturbances occur frequently in the Italian WBS population. Our data could support the existence of some "intrinsic" behavioural characteristics in WBS such as inattention and anxiety, which are detectable and important at any age; both learning and social exposure to a structured context such as school could help diminish self-absorbed behaviour. (As Provided).
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Erfasst von	ERIC (Education Resources Information Center), Washington, DC
Update	2017/4/10